Department of Congenital Heart Surgery – Pediatric Heart Surgery
Pulmonary atresia with VSD +-MAPCA (major aorto-pulmonary collaterals)
Definition
This heart defect is an extreme form of tetralogy of Fallot. The pulmonary valve is closed. The native pulmonary artery tree many be normal, hypoplastic or not present at all. The procedure is then performed via the dilated bronchial arteries.