Pulmonary atresia with intact ventricular septum


The presence of the heart defect represents the indication for an intervention/operation. The timing of the procedure depends on the:

  • stage of development of the native pulmonary artery vessel bed (really pulmonary arteries)
  • size of the right ventricle (inlet, muscular, outlet components?, tricuspid valve ring)
  • presence of right-ventricular-dependent myocardial perfusion with proximal coronary stenoses (sinusoids).